Journal of Pediatrics and Palliative Care
Congenital Diaphragmatic Hernia and Pulmonary Vein Obstruction
- 1Department of Neonatology, UZ Leuven, Belgium
- 2Department of Neonatology, AZ Sint-Lucas, Brugge, Belgium
- 3Division Pediatric Cardiology, UZ Leuven, Belgium
- 4Division Thoracic Surgery, UZ Leuven, Belgium
Tine François, Department of Neonatology, UZ Leuven, Herestraat 49, 3000 Leuven, Belgium, E-mail: email@example.com
François, T., et al. Congenital Diaphragmatic Hernia and Pulmonary Vein Obstruction. (2016) J Palliat Care Pediatr 1(1): 13- 17.
© 2016 François, T. This is an Open access article distributed under the terms of Creative Commons Attribution 4.0 International License.
KeywordsCongenital diaphragmatic hernia; Pulmonary hypertension; Pulmonary venous hypertension; Pulmonary vein obstruction; Pulmonary vein stenosis
Persistent pulmonary hypertension of the newborn is a common complication of congenital diaphragmatic hernia (CDH).This research describes two cases of right-sided CDH (R-CDH) with a sudden late onset of rapidly progressing and eventually fatal pulmonary vein obstruction. The pathophysiology of pulmonary hypertension (PHT) in CDH and PHT in addition to pulmonary vein stenosis, and the possible differences between R-CDH and left-sided congenital diaphragmatic hernia (L-CDH) are examined and correlated to the presented case histories.