International Journal of Neurology and Brain Disorders
- 1Department of Neurology, Federal Fluminense University, HUAP, Niterói, Rio de Janeiro, Brazil
- 2Department of Neurology, São Paulo Federal University, UNIFESP, São Paulo, SP, Brazil
- 3Undergraduate of Medicine Federal Fluminense University, Rio de Janeiro, Brazil
- 4Undergraduate of Medicine, Federal Fluminense University, Rio de Janeiro, Brazil
- 5Federal University, Piaiu UFPI, Parnaiba, Brazil
Marco Orsini, Masters Program in Science Rehabitation, Department of Neurology, Bonsucesso, Rio de Janeiro, Brazil. E-mail: firstname.lastname@example.org
Orsini, M., et al. Hirayama’s Disease: Case Report ( 2015) Int J Neurol Brain Disord 2(2): 1- 3.
©2015 Orsini, M. This is an Open access article distributed under the terms of Creative Commons Attribution 4.0 International License.
Keywordslower motor neuron, monomelic amyotrophy, Hirayama disease, spinal muscular atrophy.
The Hirayama's disease affects the neurons of the anterior horn of the spinal cord, usually C7 -T1 in young individuals, which causes weakness of the distal muscles of the upper limbs. We report a case of a 14 years old patient presented with significant left hand weakness associated with difficultygripping objects. After performing a resonance of the cervical spine, there were few hyperintense signalsin the anterior horn at the C5-C6 segment. In this situation we can differentiate this case from other conditions, making the correct diagnosis. It is important to report it due to the necessity of better methods that can perform the diagnosis.